Abstract
Supernumerary nostril is considering a rare congenital craniofacial disorder, which includes two additional nostrils without upper respiratory communication, as the case in this study, where three nostrils were located at the medial lineal, whether the fourth nostril was located near the right eye. All cavities were around 3 mm diameter and one accessory upper lateral cavity around 5 mm. Two cavities were lined with mucous membrane and filled with mucoid discharge. Nasal endoscopy of cavities showed that they were small as compared to a normal nasal cavity and only two communicate with upper air respiratory system. Normal cytogenetic analysis was observed 46XX. The supernumerary nostrils may occur due to an alteration to the homebox genes, taking in consideration that morphogenesis depends on these genes integrity during fetal growth.